A. Khandelwal, V. Tandon, A.K. 58-61. Background Split cord malformations (SCMs) are uncommon congenital anomalies. Frequently with overlying cutaneous and/or subcutaneous abnormalities. 1992 Sep;31(3):451-80. SUMMARY: We present a variant of a split cord malformation with coexisting segmental spinal dysgenesis. Usually, the cord is split by some type of mesenchymal derivative such as bone or cartilage. Two days after birth micro-neurosurgery was performed. DISCUSSION. MRI of whole spine and brain was done. Normally, only the spinal cord passes through this opening. Type 1. The term is from the Greek "diastema" (cleft) and "myelos" (marrow or medulla). Introduction. 1993; 33:374–8. Type 1—which may not cause symptoms—is the most common form of CM. The split lengths of the 19 Type I lesions (including the one case of double bone spurs and tripartite cord, in which the two split lengths were identical) varied between 1 and 7 vertebral levels, with a mean of 2.97. MahapatraAn unusual case of 4 level spinal dysraphism: multiple composite type 1 and type 2 split cord malformation, dorsal myelocystocele and hydrocephalous. Cranial and cervical MRI showed Chi-ari I and corpus callosum hypoplasia. Type I Split Cord Malformation. In type I, the two hemicords are typically separated by a fibrous, cartilaginous, or osseous septum and reside in two separate dural tubes (Figure 7). Chiari malformation type 1 is a structural abnormality of the cerebellum, the part of the brain that controls balance, and the skull. 14. 13. It has reported an uncommon case a 3 year-old girl a composite split cord malformation (SCM) with two different levels of SCM type1 and one level SCM type2, tight filum and sacral dermal sinus. The dorsolumbar and lumbar regions were the most common sites. L5 and S1), split cord malformation type I which separated two hemi-cords, tethered cord and syringomyelia. The split spinal cord malformation (SSCM) is an uncommon congenital malformation of the vertebral canal in which parts of the spinal cord are longitudinally duplicated. In the SSCM Type II, both parts of the spinal cord are surrounded by a common dura tube. The differential diagnosis includes dimyelia (complete spinal cord duplication) and diplomyelia (the presence of an accessory spinal cord). Split spinal cord malformation Synonyms: Diastematomyelia, SSCM, Diplomyelia, Pseudodiplomyelia, Dimyelia, Split cord malformation, SCM type 1, Split cord malformation type 1 Back to top A Type I SCM consists of two hemicords, each contained within its own dural tube and separated by a dura-sheathed rigid osseocartilaginous median septum. Figure A is an axial T2-weighted image at the T12 level demonstrating diastematomyelia with two hemicords sharing a single … The split lengths of the 18 single Type II lesions varied between 0.5 and 2 vertebral levels, with a mean of 1.17. The complete or partial division of the spinal cord is due to the presence of a septum in the central part of the spinal canal. Surgical management of adult Type 1 split cord malformation. Preoperatively the patient had paraparesis and discretely moved his left foot. The excision of bony spur in type 1 split cord malformation is challenging due to the intricate pathologic anatomy. The split spinal cord is a rare congenital malformation. Five out of nine patients that had preoperative bladder dysfunction were improved. Neurosurgery. It is the most common type. Background Split cord malformation (SCM) remains an important cause of tethered cord syndrome. Warder DE, Oakes WJ. Diastematomyelia (occasionally diastomyelia) is a congenital disorder in which a part of the spinal cord is split, usually at the level of the upper lumbar vertebra.. Diastematomyelia is a rare congenital anomaly that results in the "splitting" of the spinal cord in a longitudinal direction.Females are affected much more commonly than males. Conclusion. Neurosurgery. DIASTEMATOMYELIA or split cord malformation is a rare phenomenon that may be discovered on magnetic resonance imaging of the spine. Chiari malformation Type I Type 1 happens when the lower part of the cerebellum (called the cerebellar tonsils) extends into the foramen magnum. [Google Scholar] 34. Whereas, in Type II split cord malformations both the hemicords lie withina single, non-duplicated, dural tube[2]. This has often (but not consistently) been referred to as diastematomyelia. MahapatraAn unusual case of split cord malformation with … The malformation occurs when the lower part of the cerebellum extends below the foramen magnum (the large hole at the base of the skull which allows passage of the spinal cord), without involving the brainstem. Indian J Pediatr. There were 88 girls (73 %) and 43 boys (27 %). Type 1.5 split cord malformation? Rev Neurol (Paris). This septum can be formed out of bone tissue or it can be cartilaginous or fibrous. 2017. [Google Scholar] 33. The female predominance was slightly more remarkable in type I SCMs than in type II SCMs. View Record in Scopus Google Scholar. Tethered cord syndrome and the conus in a normal position. The difference is statistically significant There are 4 types of Chiari malformation depending on the part of the brain that is pushed down into the spinal canal. A. Agarwal, A. Raheja, S.A. Borkar, A.K. There was no hydrocephalus. Wolf AL, Tubman DE, Seljeskog EL. Type I split cord malformation Final Diagnosis. Management of split cord malformation in children: the Lyon experience. Compared with Type II SCM, patients with Type I SCM presented with higher incidence of kyphotic deformity, more extensive and complicated vertebral anomalies, and more complex rib anomalies. 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